Spinal muscular atrophy Clinical Trials

19 Active Trials

NCT05861999

A Study Evaluating the Effectiveness and Safety of Risdiplam Administered in Pediatric Patients With Spinal Muscular Atrophy Who Experienced a Plateau or Decline in Function After Gene Therapy

This is an open-label, single-arm, multicenter clinical study to evaluate the effectiveness and safety of risdiplam administered in pediatric participants with SMA and 2 SMN2 copies who previously received onasemnogene abeparvovec and experience a plateau or decline in function. Participants to be enrolled are children \<2 years of age genetically diagnosed with SMA.

RECRUITING PHASE4
Sponsor Hoffmann-La Roche
Enrollment 28
Start Date 08-14-2024
Interventions Risdiplam
NCT05861986

A Study Evaluating the Effectiveness and Safety of Risdiplam Administered as an Early Intervention in Pediatric Participants With Spinal Muscular Atrophy After Gene Therapy

This is an open-label, single-arm, multicenter clinical study to evaluate the effectiveness and safety of risdiplam administered as an early intervention in pediatric participants with spinal muscular atrophy (SMA) and 2 SMN2 copies who have previously received onasemnogene abeparvovec. Participants are children \< 2 years of age genetically diagnosed with SMA.

RECRUITING PHASE4
Sponsor Hoffmann-La Roche
Enrollment 28
Start Date 05-30-2024
Interventions Risdiplam
NCT07448610

ASsessing The REAl-world Safety & Effectiveness of Spinal Muscular Atrophy Participants Treated With Intrathecal Onasemnogene Abeparvovec-brve (OAV101B) (ITVISMA®): A U.S. Pragmatic Multicenter Study (STREAM)

The primary purpose is to address critical evidence in the treatment landscape for Spinal Muscular Atrophy (SMA), specifically focusing on the intrathecal formulation of onasemnogene abeparvovec-brve (ITVISMA®). U.S. Pragmatic Multicenter Study (STREAM).

NOT_YET_RECRUITING PHASE4
Sponsor Novartis Pharmaceuticals
Enrollment 36
Start Date 07-01-2026
Interventions Onasemnogene Abeparvovec-brve
NCT03505099

Pre-Symptomatic Study of Intravenous Onasemnogene Abeparvovec-xioi in Spinal Muscular Atrophy (SMA) for Patients With Multiple Copies of SMN2

To evaluate the safety and efficacy of intravenous onasemnogene abeparvovec-xioi in pre-symptomatic patients with SMA and 2 or 3 copies SMN2

COMPLETED PHASE3
Sponsor Novartis Gene Therapies
Enrollment 30
Start Date 04-02-2018
Interventions onasemnogene abeparvovec-xioi
NCT03381729

Study of Intrathecal Administration of Onasemnogene Abeparvovec-xioi for Spinal Muscular Atrophy

The purpose of this trial is to evaluate the safety and tolerability of intrathecal administration of onasemnogene abeparvovec-xioi in infants and children with Spinal Muscular Atrophy with 3 copies of SMN2 and deletion of SMN1.

TERMINATED PHASE1
Sponsor Novartis Gene Therapies
Enrollment 32
Start Date 12-14-2017
Interventions Onasemnogene Abeparvovec-xioi
NCT05335876

Long-term Follow-up of Patients With Spinal Muscular Atrophy Treated With OAV101 in Clinical Trials

This is a global, prospective, multi-center study that is designed to assess the long-term safety and efficacy of OAV101 in patients who participated in an OAV101 clinical trial. The assessments of safety and efficacy in Study COAV101A12308 will continue for 5 years after enrollment in this study.

RECRUITING PHASE3
Sponsor Novartis Pharmaceuticals
Enrollment 175
Start Date 12-19-2022
Interventions onasemnogene abeparvovec
NCT05089656

Efficacy and Safety of Intrathecal OAV101 (AVXS-101) in Pediatric Patients With Type 2 Spinal Muscular Atrophy (SMA)

This was a Phase III multi-center, single dose (1.2 x 10\^14 vector genomes), randomized, sham controlled, double-blind study that investigates the efficacy, safety and tolerability of OAV101B in treatment naive, sitting and never ambulatory SMA patients 2 to \<18 years of age.

COMPLETED PHASE3
Sponsor Novartis Pharmaceuticals
Enrollment 126
Start Date 02-01-2022
Interventions OAV101, Sham control
NCT05386680

Phase IIIb, Open-label, Multi-center Study to Evaluate Safety, Tolerability and Efficacy of OAV101 Administered Intrathecally to Participants With SMA Who Discontinued Treatment With Nusinersen or Risdiplam

This was a Phase IIIb open-label, single arm, multi-center study to evaluate the safety, tolerability and efficacy of OAV101B in participants with SMA aged 2 to \<18 years after the discontinuation of treatment with nusinersen or risdiplam. The study aimed to enroll approximately 28 participants across each of 2 age brackets (2 to \<6 years, and 6 to \<18 years).

COMPLETED PHASE3
Sponsor Novartis Pharmaceuticals
Enrollment 27
Start Date 01-12-2023
Interventions OAV101
NCT05152823

Gene Therapy for IGHMBP2-Related Diseases

Open-label, single intrathecal injection study of a AAV9 vector carrying the IGHMBP2 gene for IGHMBP2-related diseases.

ENROLLING_BY_INVITATION PHASE1 / PHASE2
Sponsor Megan Waldrop
Enrollment 10
Start Date 11-04-2021
Interventions Gene Therapy
NCT04833348

Quantification of Motor Function in Infants With Spinal Muscular Atrophy Treated With Innovative Therapies

The aim of the study is to propose a method for quantifying motor function in infants with spinal muscular atrophy treated with innovative therapies using inertial sensors.

ACTIVE_NOT_RECRUITING NA
Sponsor Assistance Publique - Hôpitaux de Paris
Enrollment 35
Start Date 03-20-2021
Interventions Motor function measurement using inertial sensors
NCT06288230

An Open Label Study of Gene Therapy Product (Vesemnogene Lantuparvovec) in Spinal Muscular Atrophy

This is an interventional study to evaluate safety and efficacy of AAV-hSMN1 in spinal muscular atrophy patients.

RECRUITING PHASE1 / PHASE2
Sponsor Lantu Biopharma
Enrollment 20
Start Date 10-20-2024
Interventions vesemnogene lantuparvovec
NCT05824169

Evaluation of Safety and Efficacy of Gene Therapy Drug in the Treatment of Spinal Muscular Atrophy (SMA) Type 1 Patients

The study will evaluate safety and efficacy of intrathecal delivery of GC101 gene therapy drug as a treatment of spinal muscular atrophy Type 1 (SMA 1) patients.

RECRUITING PHASE1 / PHASE2
Sponsor GeneCradle Inc
Enrollment 18
Start Date 02-25-2023
Interventions GC101
NCT06421831

Evaluation of Safety and Efficacy of Gene Therapy Drug in the Treatment of Spinal Muscular Atrophy (SMA) Type 3 Patients

The study will evaluate safety and efficacy of intrathecal delivery of GC101 gene therapy drug as a treatment of spinal muscular atrophy Type 3 (SMA 3) patients.

RECRUITING PHASE1 / PHASE2
Sponsor GeneCradle Inc
Enrollment 21
Start Date 05-10-2024
Interventions GC101
NCT05901987

Evaluation of Safety and Efficacy of Gene Therapy Drug in the Treatment of Spinal Muscular Atrophy (SMA) Type 2 Patients

The study will evaluate safety and efficacy of intrathecal delivery of GC101 gene therapy drug as a treatment of spinal muscular atrophy Type 2 (SMA 2) patients.

ACTIVE_NOT_RECRUITING PHASE1 / PHASE2
Sponsor GeneCradle Inc
Enrollment 33
Start Date 08-01-2023
Interventions GC101
NCT06971094

Safety and Efficacy Evaluation of GC101 Gene Therapy Via Intrathecal (IT) Injectionin the Treatment of Patients With Type 2 Spinal Muscular Atrophy (SMA) - Phase III

This trial employs a multicenter, randomized, open-label, standard-of-care-controlled design and plans to enroll 50 patients with Type 2 SMA aged 2 to 12 years who have previously received nusinersen. The primary objective of the trial is to evaluate the efficacy of GC101 in treating Type 2 SMA. The secondary objectives are to assess the efficacy, safety, and pharmacokinetic (PK) profile of GC101 in treating Type 2 SMA.

RECRUITING PHASE3
Sponsor GeneCradle Inc
Enrollment 50
Start Date 05-27-2025
Interventions GC101 adeno-associated virus injection
NCT06888661

Clinical Trial to Assess the Safety and Efficacy of EXG001-307 in Patients With Spinal Muscular Atrophy

The purpose of this trial is to evaluate safety and efficacy of intrathecal delivery of EXG001-307 as a treatment of spinal muscular atrophy .

ENROLLING_BY_INVITATION EARLY_PHASE1
Sponsor Guangzhou Jiayin Biotech Ltd
Enrollment 4
Start Date 03-10-2025
Interventions EXG001-307 injection
NCT04851873

Safety and Efficacy of Intravenous OAV101 (AVXS-101) in Pediatric Patients With Spinal Muscular Atrophy (SMA)

To evaluate the safety, tolerability and efficacy of intravenous administration of OAV101 (AVXS-101) in patients with spinal muscular atrophy (SMA) with bi-allelic mutations in the survival motor neuron 1 (SMN1) gene weighing ≥ 8.5 kg and ≤ 21 kg, over a 12 month period.

COMPLETED PHASE3
Sponsor Novartis Pharmaceuticals
Enrollment 24
Start Date 09-08-2021
Interventions OAV101
NCT05073133

Safety and Efficacy of Intravenous OAV101 (AVXS-101) in Pediatric Patients With Spinal Muscular Atrophy (SMA) (OFELIA)

This was a phase IV Open-label, single-arm, single-dose, multicenter study, to evaluate the safety, tolerability and efficacy of intravenous administration of OAV101 (AVXS-101) in patients with SMA with bi-allelic mutations in the survival motor neuron 1 (SMN1) gene ≤ 24 months and weighing ≤ 17 kg, over a 18-month period post infusion.

COMPLETED PHASE4
Sponsor Novartis Pharmaceuticals
Enrollment 16
Start Date 11-04-2021
Interventions OAV101
NCT02122952

Gene Transfer Clinical Trial for Spinal Muscular Atrophy Type 1

The purpose of this trial is to evaluate safety and efficacy of intravenous delivery of AVXS-101 as a treatment of spinal muscular atrophy Type 1 (SMN1).

COMPLETED PHASE1
Sponsor Novartis Gene Therapies
Enrollment 15
Start Date 05-05-2014
Interventions AVXS-101

Data sourced from ClinicalTrials.gov. Last updated: April 14, 2026